Year
Trial
Title / pubmed.gov
Journal
Sarcoma Subtype
First Author
2021
Cancer
Ewing Sarcoma
Chugh
2020
Journal of Geriatric Oncology
Locally advanced or metastatic soft tissue sarcoma
Younger
2020
The Oncologist
Refractory Liposarcoma
Riedel
2020
Clinical Cancer Research
Undifferentiated Pleomorphic Sarcoma and Poorly Differentiated/
Dedifferentiated Liposarcoma
Keung
2020
Nature
Undifferentiated Pleomorphic Sarcoma and Poorly Differentiated/
Dedifferentiated Liposarcoma
Petitprez
2019
Sarcoma
Metastatic Leiomyosarcoma
Choy
2019
Journal of Clinical Oncology
Osteogenic Sarcoma
Davis
2018
JAMA Oncology
Advanced Gastrointestinal Stromal Tumors
Schuetze
2018
Sarcoma
Metastatic Leiomyosarcoma
Choy
2017
Sarcoma
Malignant peripheral nerve sheath tumors sporadic or NF1 associated
Higham
2017
Cancer
Alveolar soft part sarcoma, chondrosarcoma, chordoma, epithelioid sarcoma, or solitary fibrous tumor
Schuetze
2017
The Lancet, Oncology
Locally advanced or metastatic soft tissue sarcoma
Tap
2017
The Lancet, Oncology
Undifferentiated Pleomorphic Sarcoma and Poorly Differentiated/
Dedifferentiated Liposarcoma
Tawbi
2016
Cancer
Leiomyosarcoma, liposarcoma, MFH/pleomorphic undifferentiated sarcoma, rhabdomyosarcoma, malignant peripheral nerve sheath tumor, osteosarcoma (skeletal or extraosseous), chondrosarcoma, ewing’s, alveolar soft part sarcoma, chordoma, epithelioid sarcoma, giant cell tumor of bone, hemangiopericytoma/
solitary fibrous tumor, gastrointestinal stromal tumors (GIST)
Schuetze
2016
Journal of Clinical Oncology
Ewing’s sarcoma, osteosarcoma, synovial sarcoma, rhabdomyosarcoma, alveolar soft part sarcoma, desmoplastic small round cell tumor, extraskeletal myxoid chondrosarcoma, clear cell sarcoma
Koshkin
2014
Cancer
Ewing’s sarcoma, osteosarcoma, synovial sarcoma, rhabdomyosarcoma, alveolar soft part sarcoma, desmoplastic small round cell tumor, extraskeletal myxoid chondrosarcoma, clear cell sarcoma
Pappo
2013
Adjuvant therapy for high-grade, uterus-limited leiomyosarcoma: results of a phase 2 trial (SARC005)
Cancer
Uterine Leiomyosarcoma
Hensley
2012
The Oncologist
Recurrent Ewing’s Sarcoma, Osteosarcoma, or Unresectable or Locally Recurrent Chondrosarcoma
Fox
2010
Clinical Cancer Research
Desmoid tumors
Chugh
2009
Journal of Clinical Oncology
Ewing’s Family (including PNET), OsteosarcomaSynovial Sarcoma, Leiomyosarcoma, Rhabdomyosarcoma (including alveolar, embryonal and pleomorphic), Liposarcoma (all variants), Malignant Fibrous Histiocytoma, Peripheral Nerve Sheath (including MPNST, neurofibrosarcom, schwannoma), Fibrosarcoma, Angiosarcoma (all variants), Desmoid Tumor, GI Stromal (c-kit negative only)
Chugh
2007
Journal of Clinical Oncology
Unresectable soft tissue sarcoma
Maki